Francisca Rodríguez Escobar¹, Cristóbal Arroyo Zambrano², Manuel Alvarez Vaccaro³ and Alejandro Alvarez Jara⁴*

¹Physician-surgeon, Cesfam San Pedro de la Paz Concepción, Chile
²Medical student, Faculty of Medicine Universidad Católica de la Santísima, Concepción, Chile
³Medical student, Faculty of Medicine Universidad del Desarrollo Santiago, Chile
⁴Pediatrician and Pediatric Cardiologist, Fetal Exploration Unit Hospital Guillermo, Grant Benavente Concepción, Chile

*Corresponding Author: Alejandro Alvarez Jara, Pediatrician and Pediatric Cardiologist, Fetal Exploration Unit Hospital Guillermo, Grant Benavente Concepción, Chile.

Received: September 26, 2023; Published: October 24, 2023

Abstract

Rhabdomyoma corresponds to the most common fetal cardiac tumor, and can affect any point of the cardiac muscle, generating various manifestations. Very large tumors can cause hemodynamic obstruction, requiring surgery.

Its development is related to tuberous sclerosis, which produces abnormal cell proliferation, which is why sirolimus, a rapamycin (mTOR) inhibitor, has been used for its antitumor activity. A clinical case is presented where the cardiac rhabdomyoma, despite generating great obstruction in the outlet of the left ventricle, was completely resolved after the administration of sirolimus, without generating adverse effects or the need for surgery.

Keywords: Rhabdomyoma; Cardiac Tumor; Prenatal Diagnosis

References

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Citation

Citation: Alejandro Alvarez Jara.,et al. “Fetal Rhabdomyoma: Case Report".Acta Scientific Nutritional Health 7.11 (2023): 21-23.

Copyright

Copyright: © 2023 Alejandro Alvarez Jara.,et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.