Noura Zohir Mahmoud* and Ihab Saad Othman

Eye World Hospital, Giza, Egypt

*Corresponding Author: Noura Zohir Mahmoud, Eye World Hospital, Giza, Egypt.

Received: April 14, 2024; Published: January 09, 2025

Abstract

An isolated astrocytic hamartoma of the optic nerve head (ONH) is a rare entity that can present without associated systemic manifestations or other retinal findings. We report a unique case involving a 36-year-old Yemeni male who presented with rapid and progressive right eye vision loss. Comprehensive ophthalmic and systemic evaluations were performed. Fundus examination revealed an ONH mass with calcification, while fundus fluorescein angiography (FFA) demonstrated late leakage from the optic disc lesion. B-scan ultrasonography and optical coherence tomography (OCT) further characterized the ONH calcifications. The diagnosis was made presumptively based on clinical findings and exclusion of other conditions, including tuberous sclerosis complex (TSC). Informed consent was obtained from the patient prior to documenting this case.

Keywords: Astrocytic Hamartoma; Optic Nerve Head; Multimodal Imaging; OCT; FAF; AHONH

References

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Citation

Citation: Noura Zohir Mahmoud and Ihab Saad Othman. “Navigating Diagnostic Challenges: An Isolated Optic Nerve Head Astrocytic Hamartoma: A Case Report". Acta Scientific Ophthalmology 8.1 (2025): 10-16.

Copyright

Copyright: © 2025 Noura Zohir Mahmoud and Ihab Saad Othman. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.