Tian Xia and Neelakshi Bhagat*
Institute of Ophthalmology and Visual Science, Rutgers New Jersey Medical School, Newark, New Jersey, United States
*Corresponding Author: Neelakshi Bhagat, Institute of Ophthalmology and Visual Science, Rutgers New Jersey Medical School, Newark, New Jersey, United States.
Received: May 24, 2018; Published: July 13, 2018
Citation: Tian Xia and Neelakshi Bhagat.“Mesoionic Compounds and its Application in Organic and Pharmaceutical Field”. 1.1 (2018).
Background: Facioscapulohumeral muscular dystrophy (FSHD) is an autosomal dominant disease with facial muscles weakness and scapular weakness. Ophthalmic manifestations may include retinal vasculopathy similar to Coats’ disease. We report a case of Coatslike response in FSHD which has remained stable with no exudation.
Case Presentation: A 7-years old female with Coats’- like response associated with FSHD. Fundus photos show mild tortuosity of posterior pole vasculature. Fundus angiography shows avascularity of peripheral temporal retina with telangiectatic vessels and aneurysmal dilatations of vessels at the edge of avascular retina without neovascularization or exudates.
Discussion and Conclusion: This case demonstrates a Coats-like response in a patient with FSHD that has remained stable and has not required any treatment. Other reports have demonstrated peripheral/macular exudative retinopathy, peripheral neovascularization and neovascular glaucoma.
Keywords: Coats’ Disease; Facioscapulohumeral Muscular Dystrophy
Copyright: © 2018 Tian Xia and Neelakshi Bhagat. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.