Aixa Lucia Mercé*, María Lourdes Mamani Ortega, Vanesa Marisel Bejarano and Anastasia Secco

Section of Rheumatology, Hospital B. Rivadavia, Buenos Aires

*Corresponding Author: Aixa Lucia Mercé, Section of Rheumatology, Hospital B. Rivadavia, Buenos Aires.

Received: January 09, 2023; Published: April 04, 2023

Abstract

Granulomatosis with Polyangiitis (GPA) is a clinical-pathological condition that presents with granulomatous inflammation of the upper and lower respiratory tract, focal necrotizing glomerulonephritis and necrotizing vasculitis of small and medium-sized vessels (capillaries, venules, arterioles and arteries). Orbital GPA involvement ranging from 7-45%. The lacrimal gland can occasionally be affected in isolation and be the initial manifestation of the disease. We present the case of a patient with GPA and nasolacrimal fistula.

Keywords: Granulomatosis Con Polyangiitis; Orbito-Nasal Fistula; Corneal Erosion; Nasal Septum Perforation

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Citation

Citation: Aixa Lucia Mercé., et al. “Orbito-nasal Fistula, A Therapeutic Challenge Against an Uncommon Manifestation in Granulomatosis with Polyangiitis”.Acta Scientific Medical Sciences 7.5 (2023): 12-15.

Copyright

Copyright: © 2023 Aixa Lucia Mercé., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.