Evaluation of Hemophilic Arthropathy in Children in Algiers Center
Akretche N1* and Nemmar R2
1Department of Physical Medicine and Rehabilitation, CHU Mustapha Alger Center, Algeria
2Orthopedic Surgery Department, CHU Mustapha Alger Center, Algeria
*Corresponding Author: Akretche N, Department of Physical Medicine and Rehabilitation, CHU Mustapha Alger Center, Algeria.
December 27, 2021; Published: May 27, 2022
Hemophilia is a hematological disease responsible for hemarthrosis starting from the age of learning to walk. In severe forms, these hemarthrosis are at the origin of hemophilic arthropathy that can lead to a loss of autonomy. The clinical and radiological evaluation of this arthropathy must be supplemented by a functional evaluation which will determine the impact of the disorders on the performance of activities of daily living and guide the therapeutic decision. The aim of the present work was to evaluate hemophilic joints clinically, radiologically, and functionally in patients with hemophilic arthropathy.
Our study concerned 43 patients with mean age of 9.17 +/-6.26 a total of 67 affected joints were assessed clinically by the Pednet score, radiologically by the Pettersson score and the functional FISH score. The knees are the most common joints followed by the eblows and ankles. There was a highly significant correlation between Pednet clinical score and Pettersson radiological score (P<0.00001, r = 0.769) and between Pednet clinical score and FISH functional score (r = 0.03 and P = 0.023).Given the signifiant correlation between these scores,these scores can be extremely useful in clinical practice to detect early joint damage and guide therapeutic management.
Keywords: Hemophilia; Hemophilic Arthropathy; Orthopedic Score; Radiological Score; FISH Score
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