General Pediatrician, Super Specialty Assistant (Fellowship Assistant) of Pediatric Intensive Care, Tehran University of Medical Sciences
*Corresponding Author: Mehrnoush GH, General Pediatrician, Super Specialty Assistant (Fellowship Assistant) of Pediatric Intensive Care, Tehran University of Medical Sciences.
Received: December 06, 2023; Published: December 16, 2023
Introduction: Acites is not a usual finding in prehepatic portal hypertension including portal vein thrombosis, but when portal vein thrombosis is acute and massive, ascites can be a presenting feature. A new condition of interest is protein s deficiency associated with hypercoagulation and recurrent venous thrombosis and ascites. we report the case of a non cirrhotic 9 years old male Whit tense ascites diagnosed with portal and Superior mesentric vein thrombosis caused by protein s deficiency.
Case Report: A 9 years old boy was evaluated for tense ascites which has led to um local hernia since one month before admission. he had not any clinical or laboratory stigmata of paranchymal liver disease. he had history of abdominal pain that led to appendectomy four months ago. Imaging studies showed Superior mesenteric and portal vein thrombosis. In laboratory tests for pre thrombotic states he suffered from significant proteins deficiency.
Discussion: thrombophilic states like as proteins deficiency predispose patient to vascular thrombosis. This vascular thrombosis can be present with signs and symptoms related to their territories. This is essential to prevent advancement of thrombosis or rethrombosis in patient with inherited coagulation disorders in which lifelong anticoagulation therapy is recommended.
Keywords: Protein; Deficiency; Portal Vein Thrombosis; Ascites
Citation: Mehrnoush GH., et al. “Tens Ascites as a Presentation of Proteins Deficiency".Acta Scientific Paediatrics 7.1 (2024): 16-18.
Copyright: © 2024 Mehrnoush GH., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.