Abstract

Mentosternal dysraphia is a congenital abnormality of the anterior part of the neck. It is rare and little known, and accounts for less than 2% of all cervical congenital malformations. The embryological origin is not fully elucidated. The embryologic origin is not fully understood and is thought to be the consequence of a defect in the median mesodermal fusion of the first and second gill arches between the 3^rd and 4^th week of embryonic development. It corresponds to strained flanges between the chin and the sternum. Its diagnosis is clinical and no further examination is necessary. The treatment is surgical and must be done during the first months of life to avoid mechanical and infectious complications mainly. Pediatricians, dermatologists and ENT specialists must recognize these lesions at an early stage to allow early and appropriate management. We report the observation of a newborn with mento-sternal dysgraphia diagnosed and operated on in our health establishment. The objective of this work is to study the clinical aspect, the modalities of therapeutic management and the evolution of this exceptional congenital malformation.

Keywords: Congenital Malformation; Mento-Sternal Dysgraphia

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Citation

Citation: A Badre., et al. “Mentosternal Dysraphia: A Case Report”. Acta Scientific Paediatrics 3.11 (2021): 30-32.

Copyright

Copyright: © 2021 A Badre., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.