Acta Scientific Paediatrics (ISSN: 2581-883X)

Case Report Volume 4 Issue 1

An Unexpected Outcome of Congenital Intrahepatic Arterioportal Fistula with Trisomy 21

Aktas Selma1* and Nur Seyma Zengin2

1Acibadem University Medical Faculty, Department of Pediatrics, Division of Neonatology, Turkey
2Gaziosmanpasa Taksim Research and Training Hospital, Turkey

*Corresponding Author: Selma Aktas, Acibadem University Medical Faculty, Department of Pediatrics, Division of Neonatology, Turkey.

Received: November 16, 2020; Published: December 10, 2020

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Abstract

  Congenital intrahepatic arterioportal fistula is a rare condition and presents with symptoms of portal hypertension. Congenital cardiac anomalies are common among children with Trisomy 21 and there is also an association between Trisomy 21 and congenital vascular malformations of the liver. We discuss a patient with Trisomy 21 that presented with continuous murmur in the right upper quadrant of abdomen, thrombocytopenia and mild pulmoner hypertension and diagnosed as congenital intrahepatic arterioportal fistula by doppler USG and angiography. Surprisingly the shunt regressed spontaneously without any intervention.

Keywords: Trisomy 21; Congenital İntrahepatic Arterioportal Fistula

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Citation

Citation: Aktas Selma and Nur Seyma Zengin. “An Unexpected Outcome of Congenital Intrahepatic Arterioportal Fistula with Trisomy 21". Acta Scientific Paediatrics 4.1 (2021): 06-08.




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