Joao Carvalho Pereira¹*, Andre Moreira¹, Tiago Barbosa¹, Joana Azevedo¹, Aurea Canelhas², Elisabete Ribeiro^1,2, Pedro Varanda¹ and Luis Filipe Rodrigues^1,2

¹Department of Orthopaedic and Traumatology, Hospital de Braga, Braga, Portugal
²Hospitais Trofa Saude

*Corresponding Author: Joao Carvalho Pereira, Department of Orthopaedics and Traumatology, Hospital de Braga, Braga, Portugal.

Received: March 06, 2023; Published: April 05, 2023

Abstract

Superficial Acral Fibromyxoma (SAFM) is a rare and benign soft tissue neoplasia that most often affects the digits, particularly the nail apparatus. The pathology presents as a slow-growing mass associated with xanthonychia, nail thickening, and proximal paronychia, often leading to misdiagnosis with fungal infection. The mainstay of treatment is en-bloc resection, with a non-negligible recurrence rate. This case report describes a 48-year-old female with a 2-year history of right third fingernail discoloration and thickening. After unsuccessful treatment with anti-fungal agents, longitudinal partial proximal plate nail avulsion was conducted, revealing a consistent, gelatinous and well-demarcated flesh-coloured lesion. Histopathological examination confirmed SAFM, with CD34 positivity and negativity for pS-100 immunomarkers. After 12 months of follow up, the patient was completely asymptomatic, with no signs of lesion recurrence or nail dystrophia. Minimally damaging techniques as the one described in this case report should be preferred in order to preserve the maximum amount of nail matrix and provide the best clinical results for the patient. Awareness of this rare entity and its characteristic presentation is crucial for accurate diagnosis and timely surgical management

Keywords: Superficial Acral Fibromixoma, Benign Neoplasms, Surgical Technique

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Citation

Citation: Joao Carvalho Pereira., et al. “Superficial Acral Fibromixoma-A Rare Entity, A Novel Surgical Aproach” Acta Scientific Orthopaedics 6.5 (2023): 11-13.

Copyright

Copyright: © 2023 Joao Carvalho Pereira., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.