Ahmed Alharbi¹* and Osama Samargandi²

¹Department of Head and Neck Surgery and Ear, Nose and Throat, Faculty of Medicine, King Abdulaziz University, Jeddah, Saudi Arabia
²Division of Plastic and Reconstructive Surgery, Department of Surgery, Faculty of Medicine, King Abdulaziz University, Jeddah, Saudi Arabia

*Corresponding Author: Ahmed Alharbi, Department of Head and Neck Surgery and Ear, Nose and Throat, Faculty of Medicine, King Abdulaziz University, Jeddah, Saudi Arabia.

Received: April 20, 2022; Published: May 18, 2022

Abstract

Chondrosarcoma, a malignant neoplasm, is characterized by the formation of a cartilaginous matrix by the neoplastic cells and is associated with a high recurrence rate. Chondrosarcoma of the head and neck are rare, accounting for less than 12% of all cases of chondrosarcoma. Head and neck chondrosarcoma usually involves the maxilla and rarely affects the nasal septum, with only 50 cases reported in the literature. Most head and neck chondrosarcoma occur in people in their forties, with a slight predilection for male patients. Patients usually present with a painless swelling or nasal obstruction. Wide surgical resection is the preferred treatment for chondrosarcoma; radiotherapy and chemotherapy are usually alternative options. Few clinical series have evaluated chondrosarcoma's biological behavior and surgical outcomes involving the head and neck. Here, we report the clinicopathological characteristics of a massive nasal septal chondrosarcoma, probably the largest ever reported in a young girl, resulting in bilateral visual loss and eroding the nasal and oral cavities necessitating a tracheostomy and feeding jejunostomy. Her late presentation, combined with the unusual aggressiveness of the tumor, precluded any attempts at surgical resection.

Keywords: Chondrosarcoma; Head and Neck; Nasal Septum; Surgery

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Citation

Citation: Ahmed Alharbi and Osama Samargandi. “Chondrosarcoma of the Nasal Septum: A Case Report and Literature Review". Acta Scientific Otolaryngology 4.6 (2022): 21-26.

Copyright

Copyright: © 2022 Ahmed Alharbi and Osama Samargandi. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.