Acta Scientific Otolaryngology (ASOL) (ISSN: 2582-5550)

Case Report Volume 3 Issue 8

A Rare Bleeding Disorder and a Precious Surgery: Cochlear Implantation in a Child with Von Willebrand Disease - A Case Report

R Karthikeyan1, Akshat Kushwaha2*, Sabharisan Paramasivam2, Arun Alexander3, Sivaraman Ganesan4 and Sunil Kumar Saxena5

1Senior Resident, Department of ENT, JIPMER, Puducherry, India
2Junior Resident, Department of ENT, JIPMER, Puducherry, India
3Professor, Department of ENT, JIPMER, Puducherry, India
4Associate Professor, Department of ENT, JIPMER, Puducherry, India
5Professor and Head, Department of ENT, JIPMER, Puducherry, India

*Corresponding Author: Akshat Kushwaha, Junior Resident, Department of ENT, JIPMER, Puducherry, India.

Received: July 09, 2021; Published: July 20, 2021

Abstract

  Von Willebrand disease (vWD) is the most common inherited bleeding disorder with a prevalence of 1 percent [1,2] but only a small proportion of patients come to medical attention because of the mild nature of the bleeding symptoms. The usual clinical presentation is in the form of mucosal bleed, prolonged bleed from minor cuts or trivial trauma or menorrhagia in females [3]. VWD is due to a quantitative or qualitative deficiency in von Willebrand factor (VWF), a complex plasma protein that plays a pivotal role in the control of bleeding by the formation of a platelet plug. Clinical manifestations are highly variable and co-relate with the nature of the deficiency and accordingly, with the management. Here we are reporting one such case of vWD who underwent the major surgery of cochlear implantation.

Keywords: Von Willebrand Disease (vWD); Von Willebrand factor (VWF); Cochlear Implantation

References

  1. Von Willebrand disease (2017).
  2. What is von Willebrand Disease? | CDC. Centers for Disease Control and Prevention (2019).
  3. Laffan MA., et al. “The diagnosis and management of von Willebrand disease: a United Kingdom Haemophilia Centre Doctors Organization guideline approved by the British Committee for Standards in Haematology”. British Journal of Haematology 4 (2014): 453-465.
  4. Bharati KP and Prashanth UR. “Von Willebrand Disease: An Overview”. Indian Journal of Pharmaceutical Sciences 1 (2011): 7-16.
  5. Balasubramanian L., et al. “Effectiveness of DDAVP in Von Willebrand’s Disease”. Blood11 (2004): 4031-4031.
  6. Özgönenel B., et al. “How do you treat bleeding disorders with desmopressin?” Postgraduate Medical Journal 977 (2007): 159-163.
  7. Alperin JB. “Estrogens and surgery in women with von Willebrand’s disease”. The American Journal of Medicine 3 (1982): 367-371.

Citation

Citation: Akshat Kushwaha., et al. “A Rare Bleeding Disorder and a Precious Surgery: Cochlear Implantation in a Child with Von Willebrand Disease - A Case Report".Acta Scientific Otolaryngology 3.8 (2021): 95-97.

Copyright

Copyright: © 2021 Akshat Kushwaha., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.




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Acceptance rate34%
Acceptance to publication20-30 days
Impact Factor0.871

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