Shimaa Hussein Kotb*

Assistant Lecturer, Oral Medicine, Periodontology Department at Sphinx University, New Assuit, Egypt

*Corresponding Author: Shimaa Hussein Kotb, Assistant Lecturer, Oral Medicine, Periodontology Department at Sphinx University, New Assuit, Egypt.

Received: October 13, 2023; Published: November 20, 2023

Abstract

The early hour life of newborn is an ambiguous and challenging period in human life which need careful and intelligent monitoring to obtain better life outcomes. Pierre Robin Sequence one of the rare syndrome that is observed shortly after or before the birth. PRS is a group of malformation in the baby that develop during pregnancy. It is called a casade because one of its definite features − an undeveloped lower jaw − initiate a casade of other deformities while the baby is developing in uterus and can ultimately lead to post-natal upper airway obstruction and life threatening condition that lead to eventual death.

Aim: The purpose of the study was to highlight the significance of three-dimensional ultrasound in the screening of fetal micrognathia and highlight the diagnostic features of infant with Pierre Robin syndrome; to establish an early assessment approach for better outcomes of infant life.

Methodology: A systematic literature review depends on collecting data from an evidence based studies. Searches were made of twenty five electronic databases: the Cochrane Oral Health Group’s Trials Register, The Cochrane Central Register of Controlled Trials (CENTRAL), EMBASE, PsycINFO, Scopus and Web of science, MEDLINE (PubMed).

Results: There is a strong association between breathing difficulty, feeding difficulty in infant and the small size of mandible which affect on fetus shelf life.

Conclusion: PRS is a rare anomaly so raise the awareness to this syndrome should be increased between different physicians. Prenatal diagnosis is very important step for appropriate treatment decision by parents before delivery and to arrange with a multidisplinary team to assessment the condition postnatal to reduce the short and long term complications and treatments.

 Keywords: Birth Defects; Pierre Robin Sequence; Micrognathia; Glossoptosis; Airway Obstruction; Obstructive Sleep Apnea; Feeding Problems

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Citation

Citation: Shimaa Hussein Kotb. “Neonatal Pierre Robin syndrome (Systematic Review)”.Acta Scientific Medical Sciences 7.12 (2023): 42-46.

Copyright

Copyright: © 2023 Shimaa Hussein Kotb. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.