John R Bach1*, Louis Saporito2 and Michael Schepis3
1Professor of Physical Medicine and Rehabilitation, Professor of Neurology, Rutgers University New Jersey Medical School, USA
2Instructor of Physical Medicine and Rehabilitation, Rutgers University New Jersey Medical School, USA
3Department of Physical Medicine and Rehabilitation, Rutgers University New Jersey Medical School, USA
*Corresponding Author: John R Bach, Professor of Physical Medicine and Rehabilitation, Professor of Neurology, Rutgers University New Jersey Medical School, USA
Received: June 20, 2023; Published: July 24, 2023
Three patients with spinal muscular atrophy, who have survived 26 to 30 years by noninvasive respiratory management rather than with tracheostomy tubes, are presented. They demonstrate that tracheostomy tubes are not always necessary for long survival for these patients, even when having 0 ml of vital capacity for decades, that nasogastric tubes do not necessarily prevent effective noninvasive nasal ventilatory support, that patients can be extubated and decannulated of tracheostomy tubes even when having 0 ml of vital capacity, and that noninvasive management is preferred by patients and care providers over the use of airway tubes for ventilatory support.
Keywords: Spinal Muscular Atrophy Type 1; Noninvasive Ventilation; Noninvasive Ventilatory Support; Mechanical Insufflation Exsufflation; Prognosis
Citation: John R Bach., et al. “Spinal Muscular Atrophy (SMA) Type 1: Case Study of Decannulation”.Acta Scientific Medical Sciences 7.8 (2023): 182-186.
Copyright: © 2023 John R Bach., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.