John R Bach¹*, Louis Saporito² and Michael Schepis³

¹Professor of Physical Medicine and Rehabilitation, Professor of Neurology, Rutgers University New Jersey Medical School, USA
²Instructor of Physical Medicine and Rehabilitation, Rutgers University New Jersey Medical School, USA
³Department of Physical Medicine and Rehabilitation, Rutgers University New Jersey Medical School, USA

*Corresponding Author: John R Bach, Professor of Physical Medicine and Rehabilitation, Professor of Neurology, Rutgers University New Jersey Medical School, USA

Received: June 20, 2023; Published: July 24, 2023

Abstract

Three patients with spinal muscular atrophy, who have survived 26 to 30 years by noninvasive respiratory management rather than with tracheostomy tubes, are presented. They demonstrate that tracheostomy tubes are not always necessary for long survival for these patients, even when having 0 ml of vital capacity for decades, that nasogastric tubes do not necessarily prevent effective noninvasive nasal ventilatory support, that patients can be extubated and decannulated of tracheostomy tubes even when having 0 ml of vital capacity, and that noninvasive management is preferred by patients and care providers over the use of airway tubes for ventilatory support.

 Keywords: Spinal Muscular Atrophy Type 1; Noninvasive Ventilation; Noninvasive Ventilatory Support; Mechanical Insufflation Exsufflation; Prognosis

References

1. Bach JR. “Point: Is Non-invasive ventilation always the most appropriate manner of long-term ventilation for infants with spinal muscular atrophy type 1? Yes, almost always?” Chest 5 (2016): 962-965.
2. Bach JR. “A comparison of long-term ventilatory support alternatives from the perspective of the patient and care giver”. Chest6 (1993): 1702-1706.
3. Bach JR., et al. “Extubation of unweanable patients with neuromuscular weakness: a new management paradigm”. Chest5 (2010): 1033-1039.
4. Chiou M., et al. “Quantitation of Oxygen induced hypercapnia in respiratory pump failure”. Revista Portuguesa de Pneumologia, Portuguese Journal of Pulmonology5 (2016): 262-265.
5. Carter RE., et al. “Comparative study of electrophrenic nerve stimulation and mechanical ventilatory support in traumatic spinal cord injury”. Paraplegia 25 (1987): 86-91.
6. Bach JR., et al. “Decannulation of patients with severe respiratory muscle insufficiency: efficacy of mechanical insufflation-exsufflation”. Journal of Rehabilitation Medicine 46 (2014): 1037-1041.
7. Bach JR and Alba AS. “Intermittent abdominal pressure ventilator in a regimen of noninvasive ventilatory support”. Chest3 (1991): 630-636.
8. Bach JR. “New approaches in the rehabilitation of the traumatic high level quadriplegic”. American Journal of Physical Medicine and Rehabilitation1 (1991): 13-20.
9. Bach JR., et al. “Efficacy of mechanical insufflation-exsufflation in extubating unweanable subjects with restrictive pulmonary disorders”. Respiratory Care4 (2015): 477-483.
10. Bach JR., et al. “Decanulation of patients with severe respiratory muscle insufficiency: efficacy of mechanical insufflation-exsufflation”. Journal of Rehabilitation Medicine 46 (2014): 1037-1041.
11. Bach JR. “A comparison of long-term ventilatory support alternatives from the perspective of the patient and care giver”. Chest6 (1993): 1702-1706.
12. Bach JR., et al. “Spinal muscular atrophy type 1 quality of life”. American Journal of Physical Medicine and Rehabilitation2 (2003): 137-142.

Citation

Citation: John R Bach., et al. “Spinal Muscular Atrophy (SMA) Type 1: Case Study of Decannulation”.Acta Scientific Medical Sciences 7.8 (2023): 182-186.

Copyright

Copyright: © 2023 John R Bach., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.