Acta Scientific Medical Sciences (ASMS)(ISSN: 2582-0931)

Case Report Volume 7 Issue 3

Syndromatic Pulmonary Lymphangioleiomyomatosis

Cristhian Manuel Velásquez*

Department of Radiology and Diagnostic Imaging, Hospital Regional de Occidente, Quetzaltenango, Guatemala

*Corresponding Author: Cristhian Manuel Velásquez, Department of Radiology and Diagnostic Imaging, Hospital Regional de Occidente, Quetzaltenango, Guatemala.

Received: January 23, 2023; Published: February 02, 2023


Lymphangioleiomyomatosis (LAM) is a rare disease that predominantly affects women, especially those of childbearing age. It occurs sporadically or is associated with tuberous sclerosis complex. The case of a 25-year-old female patient is presented, with a clinical history of fever and dry cough for one month evolution, as well as facial cutaneous angiofibromas, Shagreen patches on the neck and shoulders and Koenen nail tumors on the feet.

Keywords: Lymphangioleiomyomatosis; Tuberous Sclerosis; Cutaneous Angiofibromas; Shagreen Patches; Koenen's Tumors


  1. Sharma Rohit. “Lymphangioleiomyomatosis: Radiology Reference Article”. Radiopaedia Blog RSS,org, 3 Jan. (2023).
  2. Pineda-Bocanegra José L., et al. “Pulmonary Lymphangioleiomyomatosis, a Rare Lung Disease: Presentation of a Clinical Case”. Revista Chilena De Enfermedades Respiratorias, Sociedad Chilena De Enfermedades Respiratorias.
  3. Linfangioleiomiomatosis Pulmonar | Imagen Diagnóstica - Elsevier.
  4. “American Journal of Respiratory and Critical Care Medicine”. American Journal of Respiratory and Critical Care Medicine.
  5. Author links open overlay panel John J. Bissler Person Envelope J. Chris Kingswood., et al. “Renal Angiomyolipomata”. Kidney International, Elsevier, 1 Sept. (2004).
  6. Johnson S R., et al. “European Respiratory Society Guidelines for the Diagnosis and Management of Lymphangioleiomyomatosis”. European Respiratory Society, European Respiratory Society, 1 Jan. (2010).
  7. Lymphangioleiomyomatosis: Abdominopelvic CT and US Findings - Radiology.
  8. Author links open overlay panel Chu Shan CMD., et al. “Comprehensive Evaluation of 35 Patients with Lymphangioleiomyomatosis”. Chest, Elsevier, 10 Feb. (2016).


Citation: Cristhian Manuel Velásquez. “Syndromatic Pulmonary Lymphangioleiomyomatosis”.Acta Scientific Medical Sciences 7.3 (2023): 24-28.


Copyright: © 2022 Cristhian Manuel Velásquez. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.


Acceptance rate30%
Acceptance to publication20-30 days
Impact Factor1.403

Indexed In

News and Events

  • Certification for Review
    Acta Scientific certifies the Editors/reviewers for their review done towards the assigned articles of the respective journals.
  • Submission Timeline for Upcoming Issue
    The last date for submission of articles for regular Issues is April 30th, 2024.
  • Publication Certificate
    Authors will be issued a "Publication Certificate" as a mark of appreciation for publishing their work.
  • Best Article of the Issue
    The Editors will elect one Best Article after each issue release. The authors of this article will be provided with a certificate of "Best Article of the Issue".
  • Welcoming Article Submission
    Acta Scientific delightfully welcomes active researchers for submission of articles towards the upcoming issue of respective journals.

Contact US