Cristhian Manuel Velásquez*

Department of Radiology and Diagnostic Imaging, Hospital Regional de Occidente, Quetzaltenango, Guatemala

*Corresponding Author: Cristhian Manuel Velásquez, Department of Radiology and Diagnostic Imaging, Hospital Regional de Occidente, Quetzaltenango, Guatemala.

Received: January 23, 2023; Published: February 02, 2023

Abstract

Lymphangioleiomyomatosis (LAM) is a rare disease that predominantly affects women, especially those of childbearing age. It occurs sporadically or is associated with tuberous sclerosis complex. The case of a 25-year-old female patient is presented, with a clinical history of fever and dry cough for one month evolution, as well as facial cutaneous angiofibromas, Shagreen patches on the neck and shoulders and Koenen nail tumors on the feet.

Keywords: Lymphangioleiomyomatosis; Tuberous Sclerosis; Cutaneous Angiofibromas; Shagreen Patches; Koenen's Tumors

References

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Citation

Citation: Cristhian Manuel Velásquez. “Syndromatic Pulmonary Lymphangioleiomyomatosis”.Acta Scientific Medical Sciences 7.3 (2023): 24-28.

Copyright

Copyright: © 2022 Cristhian Manuel Velásquez. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.