Acta Scientific Medical Sciences (ASMS)(ISSN: 2582-0931)

Case Report Volume 7 Issue 3

Syndromatic Pulmonary Lymphangioleiomyomatosis

Cristhian Manuel Velásquez*

Department of Radiology and Diagnostic Imaging, Hospital Regional de Occidente, Quetzaltenango, Guatemala

*Corresponding Author: Cristhian Manuel Velásquez, Department of Radiology and Diagnostic Imaging, Hospital Regional de Occidente, Quetzaltenango, Guatemala.

Received: January 23, 2023; Published: February 02, 2023

Abstract

Lymphangioleiomyomatosis (LAM) is a rare disease that predominantly affects women, especially those of childbearing age. It occurs sporadically or is associated with tuberous sclerosis complex. The case of a 25-year-old female patient is presented, with a clinical history of fever and dry cough for one month evolution, as well as facial cutaneous angiofibromas, Shagreen patches on the neck and shoulders and Koenen nail tumors on the feet.

Keywords: Lymphangioleiomyomatosis; Tuberous Sclerosis; Cutaneous Angiofibromas; Shagreen Patches; Koenen's Tumors

References

  1. Sharma Rohit. “Lymphangioleiomyomatosis: Radiology Reference Article”. Radiopaedia Blog RSS,org, 3 Jan. (2023).
  2. Pineda-Bocanegra José L., et al. “Pulmonary Lymphangioleiomyomatosis, a Rare Lung Disease: Presentation of a Clinical Case”. Revista Chilena De Enfermedades Respiratorias, Sociedad Chilena De Enfermedades Respiratorias.
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  5. Author links open overlay panel John J. Bissler Person Envelope J. Chris Kingswood., et al. “Renal Angiomyolipomata”. Kidney International, Elsevier, 1 Sept. (2004).
  6. Johnson S R., et al. “European Respiratory Society Guidelines for the Diagnosis and Management of Lymphangioleiomyomatosis”. European Respiratory Society, European Respiratory Society, 1 Jan. (2010).
  7. Lymphangioleiomyomatosis: Abdominopelvic CT and US Findings - Radiology.
  8. Author links open overlay panel Chu Shan CMD., et al. “Comprehensive Evaluation of 35 Patients with Lymphangioleiomyomatosis”. Chest, Elsevier, 10 Feb. (2016).

Citation

Citation: Cristhian Manuel Velásquez. “Syndromatic Pulmonary Lymphangioleiomyomatosis”.Acta Scientific Medical Sciences 7.3 (2023): 24-28.

Copyright

Copyright: © 2022 Cristhian Manuel Velásquez. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.




Metrics

Acceptance rate30%
Acceptance to publication20-30 days
Impact Factor1.403

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