Intravenous Leiomyomatosis of the Uterus: Case Report
Jellouli MA* and Mathis J
Department of Gynecology and Obstetrics, Biel Spitalzentrum, Switzerland
*Corresponding Author: Jellouli MA, Department of Gynecology and Obstetrics, Biel Spitalzentrum, Switzerland.
December 14, 2021; Published: January 10, 2022
Intravenous leiomyomatosis (IVL) is a benign and rare pathology, characterized by intravenous proliferation of a histologically benign smooth muscle cell. It can result in systematic complications, especially cardiac, with threatening outcomes if remained untreated.
Intravenous leiomyomatosis (IVL) is probably underestimated, due to a likely easily missed diagnosis.
Introduction: We present a case of an intravenous leiomyomatosis without extra-pelvic involvement, with a brief review of this pathology.
Case Report: A total hysterectomy and bilateral oophorectomy was planned in a 50-year-old woman was because of recurrent pelvic pain with uterus myxomatosis detected in ultrasound. During the surgery, intravenous leiomyomatosis diagnosis was not suspected. Pathological analysis confirmed the unexpected diagnosis. Later, other imaging exams were performed without detecting any extra-pelvic localization. The patient remained with no evidence of disease after 2 years of follow-up.
Conclusion: Although Intravenous leiomyomatosis is rare, it can cause serious complications. Early diagnosis followed by an appropriate treatment (Hysterectomy and oophorectomy or anti-estrogens therapy) are necessary to patient outcome. Further exams and long-term follow-up is needed to exclude systemic metastasis or recurrences.
Keywords: Intravenous Leiomyomatosis; Myomas; Uterus
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