Abstract

Dural arteriovenous (AV) fistula is a vascular malformation of the spinal cord that is usually found on the dural surface of the spinal cord and drain through the anterior or the posterior medullary vein. The incidence in the U.S population is estimated to be 5.9 women and 3.4 men per 100,000. Spinal cord edema may extend far away from the original site of the fistula. It is the most common spinal malformation, attributing to 80% of all spinal abnormalities. Spinal angiography is the diagnostic tool of choice to confirm the diagnosis of AV fistula. Patients usually present with upper motor neuron (UMN) and lower motor neuron (LMN) lesions [1]. The neurological symptoms progress gradually, including sensory and motor deficits as well as sphincter disturbances [2]. RASA 1 gene mutations is suggested to play an important role in the pathophysiology of the AV fistula [3]. Management includes surgical intervention or embolization. However, surgery is considered to be the best option, offering a 98% success rate [1].

Keywords:Spinal Dural Arterio-venous fistulae (SDAVFs); Upper Motor Neuron (UMN), Lower Motor Neuron (LMN)

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Citation

Citation: Juna Musa., et al. “Diagnostic and Treatment of Spinal Dural Arterio-Venous Fistulae: Case Report and Literature Review". Acta Scientific Medical Sciences 4.6 (2020): 03-07.

Copyright

Copyright: © 2020 Juna Musa., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.