Acta Scientific Medical Sciences (ISSN: 2582-0931)

Case Report Volume 4 Issue 3

Evaluation of Pathophysiological Characteristics in the Setting of Budd Chiari Syndrome and Renal Artery Stenosis Induced by Polycythemia Vera

Juna Musa1*, Ali Guy2, Elton Cekaj3, Erisa Kola4, Edlira Horjeti5, Ina Kola6, Carlos Rivera7 and Belinda Bejtja1

1General Practitioner, Tirana, Albania
2Clinical Instructor of Physical Medicine and Rehabilitation, New York University, School of Medicine, NYU Medical Center, USA
3Radiologist, Regional Hospital of Durres, Albania
4Pathologist, Department of Pathology and Forensic Medicine, Albania
5Family Doctor, Primary Care Center Nr. 2, Tirana, Albania
6Plastic Surgery Resident, Tirana, Albania
7Research Fellow, General Surgery Department, Metabolic and Bariatric Institute, Cleveland Clinic, Florida, USA

*Corresponding Author: Juna Musa, General Practitioner, Tirana, Albania

Received: March 18, 2020; Published: April 01, 2020

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Abstract

  Budd-Chiari syndrome is a rare life-threatening disorder caused most frequently as a complication of Polycythemia Vera [1]. BDS is caused by an obstruction of the hepatic vein outflow at the level of either the hepatic veins or the sub-diaphragmatic segment of the inferior vena cava [2]. Myeloproliferative neoplasms and chronic inflammatory diseases are the most common causes of BCS [2]. The precise location and size of the obstruction is clinically and prognostically significant as it dictates the patient’s symptoms and guides through the appropriate therapeutic management [3]. A 54-year-old female presented with Primary Erythrocytosis from Polycythemia Vera and refractory hypertension secondary to renal arterial stenosis (RAS), findings of Reno vascular occlusive disease may be primarily due to underlying PV. Radiological assessments (CT scan with IV contrast) and the clinical presentation were consistent with the diagnosis of BCS. Along with literature review; we discussed the pathological events that take place in such rare associations.

Keywords: Budd-Chiari syndrome (BCS); Inferior Vena Cava (IVC); Polycythemia Vera; Renal Artery Stenosis

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Citation

Citation: Juna Musa., et al. “Evaluation of Pathophysiological Characteristics in the Setting of Budd Chiari Syndrome and Renal Artery Stenosis Induced by Polycythemia Vera". Acta Scientific Medical Sciences 4.3 (2020): 01-04.



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