Abstract

  Budd-Chiari syndrome is a rare life-threatening disorder caused most frequently as a complication of Polycythemia Vera [1]. BDS is caused by an obstruction of the hepatic vein outflow at the level of either the hepatic veins or the sub-diaphragmatic segment of the inferior vena cava [2]. Myeloproliferative neoplasms and chronic inflammatory diseases are the most common causes of BCS [2]. The precise location and size of the obstruction is clinically and prognostically significant as it dictates the patient’s symptoms and guides through the appropriate therapeutic management [3]. A 54-year-old female presented with Primary Erythrocytosis from Polycythemia Vera and refractory hypertension secondary to renal arterial stenosis (RAS), findings of Reno vascular occlusive disease may be primarily due to underlying PV. Radiological assessments (CT scan with IV contrast) and the clinical presentation were consistent with the diagnosis of BCS. Along with literature review; we discussed the pathological events that take place in such rare associations.

Keywords: Budd-Chiari syndrome (BCS); Inferior Vena Cava (IVC); Polycythemia Vera; Renal Artery Stenosis

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Citation

Citation: Juna Musa., et al. “Evaluation of Pathophysiological Characteristics in the Setting of Budd Chiari Syndrome and Renal Artery Stenosis Induced by Polycythemia Vera". Acta Scientific Medical Sciences 4.3 (2020): 01-04.

Copyright

Copyright: © 2020 Juna Musa., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.