Abstract

  Degos’ disease, also known as “malignant atrophic papulosis” is a rare vasculopathy characterized by typical cutaneous lesions with an unknown etiology wich was first described by Dego in 1942 [1], but another case, reported in 1941 by Köhlmeier, who interpreted it as thromboangiitis obliterans of the mesenteric vessels [2] This is an arteriopathy which involves vessels of small-caliber. Dego disease mostly affects the skin. It occurs as a limited benign, cutaneous form and in a systemic variant potentially lethal multiorgan. Male to female ratio of this disease is (3:1), and a few cases of familial involvement have been reported [3-7]. In 60% of reported cases there has been an involvement of the gastrointestinal tract and other organs [8]. Up to now, fewer than 50 living patients are known worldwide, and fewer than 200 cases reported in medical literature, because it is underdiagnosed due to the rarity of this nosology [9,10]. Patients shows symptoms between of 20- 50 years; however, symtoms have been reported even as 8 months [1,6].

Keywords: Malignant Atrophic Papulosis (MAP); Pleural Effusion; Dego

References

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Citation

Citation: Fadil Gradica., et al. "Dego`S Disease with Pleural Effusion. Case Report and Review of Literature".Acta Scientific Medical Sciences 4.1 (2020): 27-30.

Copyright

Copyright: © 2020 Fadil Gradica., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.