Rose Al Bacha¹, Claude Ghorra², Joseph Bou Jaoude³ and Bassam Abboud⁴*

¹Gastroenterology Department in Nini University Hospital, Clinical educator at University of Balamand,Lebanon
²Professor of Pathology, Geitaoui Hospital, Faculty of Medicine, Lebanese University, Lebanon
³Professor of Gastroenterology and Hepatology, Lebanese University, Lebanon
⁴Professor, Department of General Surgery, Geitaoui Hospital, Faculty of Medicine, Lebanese University, Lebanon

*Corresponding Author: Bassam Abboud, Professor, Department of General Surgery, Geitaoui Hospital, Faculty of Medicine, Lebanese University, Lebanon.

Received: June 14, 2024; Published: July 09, 2024

Abstract

Introduction: The Ewing sarcoma family of tumors (ESFT) represents a group of classic Ewing’s sarcoma of bone, extra skeletal Ewing’s sarcoma (EES), Askin tumours of the chest wall and primitive neuroectodermal tumours of bone or soft tissues. However,the existence of metastatic disease is the most crucial prognostic marker. While Ewing sarcoma is primarily a bone cancer, it rarely metastasize to the pancreas with 4 reported cases in the literature.

Case presentation: We represent a case of a 38 year old male patient diagnosed with Ewing sarcoma of the bone that developed acute pancreatitis after 6 months. MRI showed a well circumscribed mass measuring 14 mm is present at the junction of the body and tail . FNA and core biopsy was positive for a small blue cell tumor and positive for CD99. These findings were consistent of extension of Ewing sarcoma. Patient was unresponsive to chemotherapy , disease progression and died. Our case emphasizes the rarity of pancreatic ES metastases, since only four previous cases have been documented in the literature. The necessity of advances in therapy is crucial.

Keywords: Ewing; Sarcoma; Pancreas; Metastasis

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Citation

Citation: Bassam Abboud., et al. “Metastasis of Ewing Sarcoma to the Pancreas: Case Report and Literature Review". Acta Scientific Gastrointestinal Disorders 7.8 (2024): 12-14.

Copyright

Copyright: © 2024 Bassam Abboud., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.