Aneez Sadhik¹*, Suhitha Gajanthody², Ashraf Ahmed³ and Harishchandra Badekila⁴

¹Assistant Professor, Department of General Surgery, Yenepoya Medical College, Derelakatte, Mangalore, India
²Assistant Professor, Department of Paediatric Surgery, Yenepoya Medical College, Derelakatte, Mangalore, India
³Associate Professor, Department of Paediatric Surgery, Yenepoya Medical College, Derelakatte, Mangalore, India
⁴Professor and HOD, Department of General Surgery, Yenepoya Medical College, Derelakatte, Mangalore, India

*Corresponding Author: Aneez Sadhik, Assistant Professor, Department of General Surgery, Yenepoya Medical College, Derelakatte, Mangalore, India.

Received: October 11, 2023; Published:November 20, 2023

Abstract

Background: Adrenocortical carcinoma might be regarded as an ultrarare disease, and it is even more rare to have a presentation as described, in an infant. The incidence is believed to be 1 to 2 per million per year, but valid data are lacking. Adrenocortical carcinoma typically presents late with a large mass. Recognition of the typical clinical, biochemical, and imaging findings is necessary for rapid diagnosis, prompt intervention, and early use of the appropriate therapy.

Case Presentation: Herein, we describe a rare case of adrenocortical carcinoma in an infant who presented with acne and pubic hair. Preoperative considerations, intra-operative technique, postoperative management, adjuvant therapies, and a brief review of the literature are discussed.

Conclusion: A multidisciplinary approach is integral in effectively diagnosing and managing adrenocortical carcinoma.

Keywords: Adrenocortical carcinoma; MRI; CT

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Citation

Citation: Aneez Sadhik., et al. “A Rare Case of Adrenocortical Carcinoma in an Infant". Acta Scientific Clinical Case Reports 4.12 (2023): 34-37.

Copyright

Copyright: © 2023 Aneez Sadhik., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.