Tanweer Iqbal*, Ahmed Mahmoud Aborahma and Ali Mohammed Al-Lehbi

Ali Allehbi Medical Center, Riyadh, Saudi Arabia

*Corresponding Author: Tanweer Iqbal, Senior Consultant internal Medicine/Nephrology, Ali Allehbi Medical Company, Riyadh, Saudi Arabia.

Received: February 23, 2022; Published: March 10, 2022

Abstract

Primary or idiopathic hypertrophic osteoarthropathy also known as pachydermoperiostosis is a rare disease characterized by clubbing of the digits, enlargement of the extremities and synovial joint effusions and a variety of skin abnormalities resulting from cutaneous hypertrophy. Other associated features are hypertrophic gastropathy, peptic ulcer and gynecomastia. Eyelid ptosis which is caused by thickened eyelids (blepharoptosis) is a less common association with this disease. We report a rare case of a patient with a complete form of pachydermoperiostosis with bilateral ptosis, clubbing, other skin manifestations and marked erythropoietin resistant anemia.

Keywords: Primary Hypertrophic Osteoarthropathy (PHOA); Clubbing; Skin Abnormalities; Erythropoietin

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Citation: Tanweer Iqbal., et al. “Primary Hypertrophic Osteoarthropathy in End Stage Renal Disease Patient with Marked Anemia. A Case Report". Acta Scientific Clinical Case Reports 3.4 (2022): 27-29.

Copyright: © 2022 Tanweer Iqbal., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.