Acta Scientific Women's Health (ASWH)

Review Article Volume 6 Issue 5

An Uncommon Case Report of Mauric Syndrome or Diabetic Glycogenosis in Girl

Rahul Hajare*

Department of Women’s Health, India

*Corresponding Author: Rahul Hajare, Department of Women’s Health, India

Received: April 10, 2024; Published: April 18, 2024

Abstract

Mauriac syndrome is an uncommon side effect of poorly controlled adolescent diabetes mellitus. We present the case of a 17-year-old patient with type 1 diabetes who was admitted to the hospital because of a serious hyper glycemic imbalance. A failure to thrive and hepatomegaly were noted during the clinical assessment. Biological investigations revealed anicteric cholestasis, severe cytolysis, and hyperglycemia. The foundation of the care was provided by insulin and hydration therapies. The etiological examination for liver dysfunction produced negative results. Biology and medicine have positively evolved. The diagnosis of hepatic glycogenesis was upheld in light of several anamnestic and clinical evidences, as well as the absence of further abnormalities linked to hepatic disorders. The outcome was elevated blood sugar. Blood transaminases were also increased. An abdominal ultrasound indicated homogeneous hepatomegaly. Viral hepatitis serology and immunological testing came back negative, and a liver biopsy confirmed the hepatocyte ballooning. Given the favorable outcomes observed during high-dose insulin treatment, the diagnosis of Mauriac syndrome was retained.

Keywords: Mauriac Syndrome; Hepatic Glycogenosis; Diabetes Mellitus; Failure to Thrive; Hepatomegaly

References

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Citation

Citation: Svetlana Dubrovina. “Postoperative Hormonal Therapy - An Effective Way to Decrease the Risk of Endometriosis Recurrence"Acta Scientific Women's Health 6.5 (2024): 16-17.

Copyright

Copyright: © 2024 Svetlana Dubrovina. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.




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Acceptance rate30%
Acceptance to publication20-30 days
Impact Factor1.278

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