Acta Scientific Neurology (ASNE) (ISSN: 2582-1121)

Case Series Volume 6 Issue 11

Hemiconvulsion Hemiplegia Syndrome with Iron Deficiency Anemia in Children: A Report of Two Cases with Review of Literature

Durgadatta Pattanyak, Raghvendra Singh Patel, Animesh Kumar and Rajniti Prasad*

Department of Paediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi

*Corresponding Author: Rajniti Prasad, Department of Paediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi.

Received: August 14, 2023; Published: October 16, 2023


Hemiconvulsion hemiplegia epilepsy (HHE) syndrome is a rare complication of prolonged focal seizures in children and usually idiopathic but may be associated with structural, infective, traumatic and degenerative diseases. We present two cases with initial presentation as left sided focal status epilepticus, later developing left sided hemiparesis with iron deficiency anemia. This is the first association of iron deficiency with hemiconvulsion-hemiplegia-syndrome illustrating the importance of testing for iron deficiency and neuroimaging in each case of status epilepticus. More importantly, these cases also raise the possibility that deficiency in iron could be a contributing factor in cases of HHE.

Keywords: Hemiconvulsion Hemiplegia Epilepsy (HHE); Febrile Seizure; Status Epilepticus; Iron Deficiency Anemia


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Citation: Rajniti Prasad., et al. “Hemiconvulsion Hemiplegia Syndrome with Iron Deficiency Anemia in Children: A Report of Two Cases with Review of Literature". Acta Scientific Neurology 6.11 (2023): 22-25.


Copyright: © 2023 Rajniti Prasad., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.


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