Manel Chalbi^1,2, Miniar Rhaiem^1,2 and Med Ali Chemli^1,2

¹Paediatric and Preventive Dentistry Department, la Rabta hospital, Tunis, Tunisia
²Laboratory of Biological Clinical and Dento-Facial Approach (ABCDF Laboratory LR12ES10), Faculty of Dental Medicine, University of Monastir, Monastir, Tunisia

*Corresponding Author: Miniar Rhaiem, Paediatric and Preventive Dentistry Department, la Rabta hospital, Tunis, Tunisia.

Received: April 27, 2023; Published: May 24, 2023

Abstract

Patients: A 13-year-old girl was referred to the paediatric dentistry and prevention department, hospital Rabta of Tunis, Tunisia with the chief complaint of unstable old prostheses. According to clinical and radiographic manifestations, the patient was diagnosed with anhidrotic ectodermal dysplasia. The treatment began with composite resin restorations on the maxillary incisors followed by placing maxillary and mandibular removable partial dentures.

Discussion: Ectodermal dysplasia is a large group of rare congenital diseases affecting the ectodermal origin tissues including sweat glands, skin, nails, hair and teeth. The frequent type is anhidrotic-hypohidrotic ectodermal dysplasia known also as Christ Siemens Touraine syndrome. It is characterized by missing teeth, hypohidrosis or anhidrosis, hypotrichosis, conic shape of teeth, everted lips, flat nose and frontal prominence. Removable dentures are the most common treatment modality reported for dental management in children with ectodermal dysplasia in order to enhance their aesthetic appearance and to overcome their masticatory, deglutition and phonation problems.

Conclusions: Early dental management should be provided to children with anhidrotic ectodermal dysplasia. It should include preventive procedures, composite resin restorations and prosthodontic rehabilitation to improve their quality of life and increases their self-esteem.

Keywords: Ectodermal Dysplasia; Oligodontia; Paediatric Dentistry; Prosthetic Rehabilitation

References

1. AlNuaimi R and Mansoor M. “Prosthetic rehabilitation with fixed prosthesis of a 5-year-old child with Hypohidrotic Ectodermal Dysplasia and Oligodontia: a case report”. Journal of Medical Case Reports 13 (2019): 329.
2. Ladda R., et al. “Prosthodontic management of hypohidrotic ectodermal dysplasia with anodontia: A case report in pediatric patient and review of literature”. Annals of Medical and Health Sciences Research 3 (2013): 277-281.
3. Fraiz FC., et al. “Hypohidrotic ectodermal dysplasia: a clinical case with a longitudinal approach”. Journal of Contemporary Dental Practice 15 (2014): 788-791.
4. Trivedi BD and Bhatia R. “Complete and removable partial prosthesis for a child with hypohidrotic ectodermal dysplasia”. International Journal of Clinical Pediatric Dentistry 6 (2013): 71-74.
5. Pigno MA., et al. “Prosthodontic management of ectodermal dysplasia: a review of the literature”. The Journal of Prosthetic Dentistry 76 (1996): 541-545.
6. Kaul S and Reddy R. “Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: case report”. Journal of Indian Society of Pedodontics and Preventive Dentistry 26 (2008): 177-1781.
7. Güler N., et al. “Hypohidrotic ectodermal dysplasia with bilateral impacted teeth at the coronoid process: a case rehabilitated with mini dental implants”. Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontology 99 (2005): E34-38.
8. Penarrocha M., et al. “Oral rehabilitation with implants in a child with hypohidrotic ectodermal dysplasia”. Medicina Oral 5 (2000): 283-286.
9. Schnabl D., et al. “Prosthetic rehabilitation of patients with hypohidrotic ectodermal dysplasia: A systematic review”. Journal of Oral Rehabilitation 45 (2018): 555-570.
10. Shigli A and Sarkar PA. “Prosthodontic management of patients with Christ-Siemens-Touraine syndrome”. BMJ Case Report 28 (2012): 2012.
11. Guckes AD., et al. “Use of endosseous implants in a 3-year-old child with ectodermal dysplasia: case report and 5-year follow-up”. Pediatric Dentistry 19 (1997): 282-285.
12. Aydinbelge M., et al. “Implants in children with hypohidrotic ectodermal dysplasia: an alternative approach to esthetic management: case report and review of the literature”. Pediatric Dentistry 35 (2013): 441-446.
13. Paulus C and Martin P. “Hypodontia due to ectodermal dysplasia: Rehabilitation with very early dental implants”. Revue de Stomatologie, de Chirurgie Maxillo-Faciale et de Chirurgie Orale 114 (2013): e5-e8.
14. Mello BZ., et al. “Mini-implants: alternative for oral rehabilitation of a child with ectodermal dysplasia”. Brazilian Dental Journal 26 (2015): 75-78.
15. Maroulakos G., et al. “Removable partial dentures vs overdentures in children with ectodermal dysplasia: two case reports”. European Archives of Paediatric Dentistry 17 (2016): 205-210.
16. Pinto AS., et al. “Prosthetic Management of a Child with Hypohidrotic Ectodermal Dysplasia: 6-Year Follow-Up”. Case Report Dentistry 2016 (2016): 2164340.
17. De Castro AMGS., et al. “Dimensional Changes in Dental Arches after Complete Dentures Rehabilitation of a Patient with Hypohidrotic Ectodermal Dysplasia: A Case Report with 18-Year Follow-Up”. Journal of Clinical Pediatric Dentistry 45 (2021): 421-427.

Citation

Citation: Miniar Rhaiem., et al. “Prosthetic Rehabilitation of a Child with Anhidrotic Ectodermal Dysplasia: A Case Report and a Review of Literature".Acta Scientific Dental Sciences 7.6 (2023): 35-39.

Copyright

Copyright: © 2023 Miniar Rhaiem., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.