Abstract

 Primitive neuroectodermal tumor (PNET) includes a wide array of lesions with varying central and peripheral nervous system having differentiating potential. It is their insidious clinical symptoms, varying locations and rarity, the accurate diagnosis of peripheral PNETs poses a challenge for clinicians. PNETs has diagnostically characteristic immunophenotypical and genetic features that distinguish them from other small round cell tumors. We recently got to treat a patient with maxillary swelling on the left side of the face, its clinical course, histopathology with immunohistochemistry correlation of this rare entity PNET is discussed.

Keywords: PNET; NSE; CD45

References

1. Arvind Krishnamurthy., et al. “Primary peripheral primitive neuroectodermal tumor of the mandible”. Annals of Maxillofacial Surgery 2 (2013): 192-194.
2. Mills SE. “Neuroectodermal neoplasms of the head and neck with emphasis on neuroendocrine carcinoma”. Modern Pathology 3 (2002): 264-278.
3. Kulkarni MM., et al. “A rare case of extra skeletal Ewing's sarcoma/primitive neuroectodermal tumor developing in maxillary sinus of an old patient”. Journal of Oral and Maxillofacial Pathology2 (2016): 330.
4. Enver Özera., et al. “Primitive neuroectodermal tumour of the mandible”. International Journal of Pediatric Otorhinolaryngology3 (2002): 257-260.
5. Masayuki Shintaku., et al. “Malignant peripheral nerve sheath tumor of small round cell type with pleomorphic spindle cell sarcomatous areas”. Pathology International 7 (2003): 478-482.
6. Arti Rameshrao Anvikar., et al. “Malignant Peripheral Nerve Sheath Tumor with Primitive Neuroepithelial Differentiation in an Adult”. International Journal of Surgical Pathology5 (2011): 511-514.
7. Votta TJ., et al. “Peripheral primitive neuroectodermal tumor associated with the anterior mandible: a case report and review of the literature”. Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontology 5 (2005): 592-597.

Citation

Citation: Mahesh KP and Karthikeya Patil. “Primitive Neuroectodermal Tumor of Maxilla - A Rare Case Report in Adult” Acta Scientific Dental Sciences 4.7 (2020): 03-05.

Copyright

Copyright: © 2020 Mahesh KP and Karthikeya Patil. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.