Neeti A Gupta¹*, Sharad M Malvadkar¹, Rahul T Chakor² and Nasreen A Siddiqui³

¹Department of Radiology, Sir JJ Hospital and Grant Medical College, India
²Topiwala National Medical College & BYL Nair Charitable Hospital, Mumbai, India
³Saboo Siddique Maternity And General Hospital, Mumbai, India

*Corresponding Author: Neeti A Gupta, Department of Radiology, Sir JJ Hospital and Grant Medical College, India.

Received: October 20, 2021; Published: November 18, 2021

Abstract

Paraneoplastic limbic encephalitis is a component of the spectrum of Paraneoplastic neurologic disorders (PNDs). It is an immune-mediated neurological condition occurring in the presence of a known remote primary. PNDs have been reported in association with multiple malignancies, the most common one being bronchial carcinoma of lung, typically the small cell variant. Paraneoplastic autoimmune encephalitis (AE) which occurs secondary to the presence of anti-N-methyl D-aspartate receptor (NMDAR) antibodies, has been associated with ovarian teratoma. It has been described as a distinct subcategory of PNDs with a potentially lethal, however, treatment responsive course. Autoimmune enteropathy (AIE) is a rare cause of intractable diarrhea. It is considered as a probable rare complication of autoimmune anti-NMDAR encephalitis.

We present and discuss a unique case of paraneoplastic limbic encephalitis in a young woman with a small ovarian dermoid, who incidentally also presented with autoimmune enteropathy and tested positive for anti-NMDAR antibodies in serum and CSF.

Keywords: NMDA; Autoimmune; Encephalitis; Enteritis; Dermoid

References

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Citation

Citation: Neeti A Gupta., et al. “Anti-NMDAR Related Autoimmune Encephalitis and Enteritis Associated with Ovarian Dermoid: A Case Report". Acta Scientific Clinical Case Reports 2.12 (2021): . Acta Scientific Clinical Case Reports 2.12 (2021): 32-34.

Copyright

Copyright: © 2021 Neeti A Gupta., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.