Andrea Ortiz-Ordoñez1*, Jaime Jara-Lalama1 and Laura Bottani1,2
1Universidad San Francisco de Quito USFQ, Colegio Ciencias de la Salud, Calle Diego de
Robles s/n y Pampite, Quito, Ecuador
2Chairman of Neurosurgery Department, Hospital Eugenio Espejo, Quito-Ecuador
*Corresponding Author: Andrea Ortiz-Ordoñez, Neurosurgery Resident, Universidad San Francisco de Quito USFQ, Colegio Ciencias de la Salud, Calle Diego de Robles s/n y Pampite, Quito, Ecuador.
Received: April 30, 2020; Published: May 22, 2020
Introduction: Intracranial nerve sheath tumors not arising from cranial nerves are extremely rare, even more, when malignant degeneration.
Case Report: Female adult presenting cerebellar syndrome and headache. Imaging showed an intracerebellar tumor and surgery was performed. Histopathology and immunohistochemistry were compatible with intracerebellar Triton tumor.
Discussion: Twenty-five malignant intracerebral nerve sheath tumors have been reported in the literature. The presented case is not associated to neurofibromatosis; it is the fourth reported intracerebellar and the first showing rhabdomyoblastic differentiation in this location.
Conclusion: Further studies are required to establish the cell origin and the best management for this entity.
Keywords: Schwann Cell; Schwannoma; Malignant Intracerebral Nerve Sheath Tumor (MINST); Intracerebellar Malignant Nerve Sheath Tumor (ICMNST); Triton Tumor; Cerebellar Neoplasms
Citation: Andrea Ortiz-Ordoñez., et al. “Intracerebellar Malignant Nerve Sheath Tumor Not Related to Cranial Nerve”. Acta Scientific Clinical Case Reports 1.5 (2020): 03-07.
Copyright: © 2020 Andrea Ortiz-Ordoñez., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.