Abstract

Introduction: Intracranial nerve sheath tumors not arising from cranial nerves are extremely rare, even more, when malignant degeneration. 

Case Report: Female adult presenting cerebellar syndrome and headache. Imaging showed an intracerebellar tumor and surgery was performed. Histopathology and immunohistochemistry were compatible with intracerebellar Triton tumor.

Discussion: Twenty-five malignant intracerebral nerve sheath tumors have been reported in the literature. The presented case is not associated to neurofibromatosis; it is the fourth reported intracerebellar and the first showing rhabdomyoblastic differentiation in this location.

Conclusion: Further studies are required to establish the cell origin and the best management for this entity.

Keywords: Schwann Cell; Schwannoma; Malignant Intracerebral Nerve Sheath Tumor (MINST); Intracerebellar Malignant Nerve Sheath Tumor (ICMNST); Triton Tumor; Cerebellar Neoplasms

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Citation

Citation: Andrea Ortiz-Ordoñez., et al. “Intracerebellar Malignant Nerve Sheath Tumor Not Related to Cranial Nerve”. Acta Scientific Clinical Case Reports 1.5 (2020): 03-07.

Copyright

Copyright: © 2020 Andrea Ortiz-Ordoñez., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.