Fadil Gradica1*, Daniela Xhemalaj1, Lutfi Lisha1, Dhimitraq Argjiri1, Alma Cani1, Fahri Kokici1 Alma Teferici1, Flora Gradica2, Perlat Kapisyzi1 and Arben Gjata3
1University Hospital "Shefqet Ndroqi", Tirana-Albania
2Public Pharmacy, Tirana-Albania
3Visceral Surgery University Center “Mother Theresa" Tirana-Albania
*Corresponding Author: Fadil Gradica, University Hospital "Shefqet Ndroqi", Tirana-Albania.
Received: November 19, 2019; Published: December 06, 2019
Degos’ disease, also known as “malignant atrophic papulosis” is a rare vasculopathy characterized by typical cutaneous lesions with an unknown etiology wich was first described by Dego in 1942 , but another case, reported in 1941 by Köhlmeier, who interpreted it as thromboangiitis obliterans of the mesenteric vessels  This is an arteriopathy which involves vessels of small-caliber. Dego disease mostly affects the skin. It occurs as a limited benign, cutaneous form and in a systemic variant potentially lethal multiorgan. Male to female ratio of this disease is (3:1), and a few cases of familial involvement have been reported [3-7]. In 60% of reported cases there has been an involvement of the gastrointestinal tract and other organs . Up to now, fewer than 50 living patients are known worldwide, and fewer than 200 cases reported in medical literature, because it is underdiagnosed due to the rarity of this nosology [9,10]. Patients shows symptoms between of 20- 50 years; however, symtoms have been reported even as 8 months [1,6].
Keywords: Malignant Atrophic Papulosis (MAP); Pleural Effusion; Dego
Citation: Fadil Gradica., et al. "Dego`S Disease with Pleural Effusion. Case Report and Review of Literature".Acta Scientific Medical Sciences 4.1 (2020): 27-30.
Copyright: © 2020 Fadil Gradica., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.