Abstract

  The fibrolipomatous hamartoma is a benign process that causes fusiform nerve enlargement as a result of the proliferation of mature fibrous perineural tissue. It is a rare disease, diagnosed mainly in children and young adults, presenting few early manifestations, eventually leading to symptoms related to nerve compression - pain, paresis and paresthesia (eg carpal tunnel syndrome) - or tumor. The gold standard method for your diagnosis is the magnetic resonance imaging - there is no need for biopsy. Thickened and low signal nerve bundles are observed, surrounded by fibrolipomatous tissue with a high T1 sign, and the pathognomonic findings of this entity. Its appearance is compared to that of a coaxial cable in the axial plane, or "spaghetti-like" in the coronal section.

Keywords: Hypesthesia; Wrist; Median Nerve; Hamartoma; Magnetic Resonance Imaging

References

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Citation

Citation: Márcio Luís Duarte., et al. “Fibrolipomatous Hamartoma – Magnetic Resonance Imaging Diagnosis”. Acta Scientific Neurology 3.3 (2020): 03-04.

Copyright

Copyright: © 2020 Márcio Luís Duarte., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.